Pressure helps blood flow through blood vessels. Hypertension occurs when this pressure gets too high. When this happens in the blood vessels in the lungs, it is called pulmonary hypertension.
As a result, the right side of the heart needs to pump harder to move blood against the pressure. If left untreated, the right side of the heart can eventually fail.
Heart and Lungs
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The blood vessels in the lungs are sensitive to oxygen. The lower the level of oxygen, the narrower the vessels become. Higher pressure will be needed to push blood through the narrow blood vessels. Pressure will also increase when there is more blood in the lungs than normal.
There are many different causes of pulmonary hypertension in children, such as:
Birth defects that affect the heart, such as
and leaky heart valves
Deformity of the chest wall (pectus excavatum)
sickle cell disease
HIVChronic lung diseaseBlood clots in the lungs
Pulmonary hypertension can also be inherited. This is called familial pulmonary hypertension. In other cases, the cause is unknown.
Factors that may increase your risk of pulmonary hypertension include: Being born with a heart defect or a deformity of the chest wallHaving certain conditions, such as scleroderma, sickle cell disease, lupus, and HIVHaving heart or lung diseaseHaving a family member with pulmonary hypertensionLiving in a high altitude
Symptoms may include: Progressive shortness of breathBlue coloring of skin around mouth, hands, and feetChest pain or pressureFast heart rateChronic coughFatigueFainting and lightheadednessAnkle or leg swelling from fluid retention
If your child has any of these symptoms, talk to the doctor right away. These symptoms may be caused by other conditions.
You will be asked about your child’s symptoms and medical history. A physical exam will be done.
Your child's bodily fluids may be tested. This can be done with blood tests.
Images may be taken of your child's bodily structures. This can be done with: Chest x-rayCT scanCardiac catheterizationEchocardiogram
Your child's lung function may be tested. This can be done with
pulmonary function tests
Most cases of pulmonary hypertension are due to another condition. In this case, the underlying cause will be treated.
If the cause cannot be determined, your child may be treated with medication, such as: Medication to lower blood pressure in the lungsAnticoagulants to prevent blood clots from formingDiuretics to help the body eliminate extra fluidNitric oxide to relax the muscles in the arteries of the lungs
Your child may also need oxygen therapy to increase the oxygen getting into the blood stream.
In severe cases, a
may be needed.
To help reduce your child’s chance of developing pulmonary hypertension, get your child proper treatment for conditions that may lead to pulmonary hypertension.
Pulmonary hypertension. Children’s Hospital Boston website. Available at:
http://www.childrenshospital.org/az/Site510/mainpageS510P0.html. Updated 2012. Accessed November 7, 2014.
Pulmonary hypertension. Cincinnati Children’s website. Available at:
http://www.cincinnatichildrens.org/health/info/heart/diagnose/ph.htm. Updated June 2014. Accessed November 7, 2014.
Last reviewed December 2015 by Kari Kassir, MD
Please be aware that this information is provided to supplement the care provided by your physician. It is neither intended nor implied to be a substitute for professional medical advice. CALL YOUR HEALTHCARE PROVIDER IMMEDIATELY IF YOU THINK YOU MAY HAVE A MEDICAL EMERGENCY. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with any questions you may have regarding a medical condition.
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